Expert Calling for British Coroners to Test for Mad-Cow

A British professor, and expert on "mad cow" disease, is calling on coroners to test  for the presence of indicators of mad-cow disease in the deceased, according to a upi.com story.  Professor John Collinge is a member of a government panel monitoring the progress of spongiform encephalopathy, or mad cow disease.  According to the report, Collinge says that "without post-mortem tests for the infection it is impossible to get accurate information on how many people in Britain may be carrying it."

164 people in Britain are confirmed to have died of Creutzfeldt-Jakob disease, the human form of mad cow.  Currently, coroners are not required to conduct tests for the presence of the infectious agent.   Understanding the breadth of the spread of the disease is an important component in designing and implementing protections from it.  If deaths due to Creutzfeldt-Jakob disease are being missed due to a lack of testing, the 164 person figure may be less reliable, and therefore less useful. 

Sporadic CJD Claims Two Of Ashland's Best Known Muscians

Within a span of seven weeks, two popular Ashland, OR musicians have died of apparent sporadic Creuzfeldt-Jacob disease (CJD).

Dead are Dave Marston, 56, and Robin Lawson, 70. The two music industry veterans made their homes and livings in the artistic Oregon city best known for its annual Shakespeare Festival, but apparently did not work together.

Marston,  a former music director of the Oregon Shakespeare Festival, artistic director of the Siskiyou Singers, band leader of the Beatles cover band Nowhere Men, leader of the Marston Family Singers (with Tami and their combined six children), The Ancient Men, the Rogue Valley Peace Choir, the Children's Peace Choir and choirs at the First Methodist Church, the Congregational Church and the Havurah Shir Hadash in Ashland.

He died June 22nd of sporadic CJD

Lawson was a jazz pianist, actor, broadcast journalist and press secretary to a U.S. Congressman. He was a British immigrant, who enlisted in the U.S. Army after studying jazz in California. He performed a long-running one man show as Winston Churchill and worked in both radio and television as a journalist.


He died Aug. 9th of sporadic CJD.

The Oregon Department of Human Services has kept track of CJD deaths for the past 18 years, and reports there have been a total of six cases in Jackson County, where Ashland is located. Not all were confirmed.

CJD is said to affect about one in a million people worldwide. The Ashland men were diagnosed with CJD by specialists at the University of California at San Francisco.

Study Suggests Chronic Wasting Disease Does NOT Jump the Species Barrier

Science Daily is reporting on results of study that suggests that people who consume deer and elk with chronic wasting disease (CWD) may be escaping infection by an inability of the infectious agent to spread to people.

Data from an ongoing multi-year study suggest that people who consume deer and elk with chronic wasting disease (CWD) may be protected from infection by an inability of the CWD infectious agent to spread to people. The results to date show that 14 cynomolgus macaques (monkeys)  exposed orally or intracerebrally to CWD remain healthy and symptom free after more than six years of observation.

The study does not yet mean it is safe for people to eat elk or deer with CWD. According to SD:

CWD is a type of brain-damaging disease known as a transmissible spongiform encephalopathy (TSE) or prion disease. CWD primarily affects deer, elk, and moose.

Other TSE diseases include mad cow disease, or bovine spongiform encephalopathy (BSE) in cattle, scrapie in sheep, and sporadic Creutzfeldt-Jakob disease (CJD) in humans. Humans are not susceptible to sheep scrapie, but BSE appears to have infected about 200 people, primarily in Europe in the 1990s. Those findings provided the rationale for the present CWD-macaque study, which began in 2003.