UK May Have Mad Cow Disease Death of 22-Year Old Man

The family of the United Kingdom's Andrew 'Rew' Hawker are confident that when test results are in, they will show he died from variant CJD---linked to eating BSE infected meat.

Hawker died at at King's Mill Hospital on 7th May after being struck down by pneumonia while he fought the degenerative neurological disorder.

The 22-year old Bilsthorpe man has died from a suspected case of the incurable Creutzfeldt-Jakob Disease (CJD) — better known as 'mad cow' disease.  Health experts have told his family Andrew suffered from the more common sporadic form of CJD which usually affects 45-75 year olds.

Hawker  was diagnosed with the brain disease in October last year and his brave fight against it touched the hearts of his devastated friends and family.

For more on this tragic death, go here.

Canada Finds 16th Animal Suffering With Mad Cow Disease Since 2003

Canada must have a blank press release for announcing when another cow is discovered with bovine spongiform encephalopathy (BSE) or Mad Cow disease.

The Canadian Food Inspection Agency (CFIA) says a six-year-old dairy cow in the western province of Alberta has been confirmed as Canada's 16th case of mad cow disease since 2003.

The CFIA says the animal tested positive for bovine spongiform encephalopathy, or BSE. No part of the carcass entered the human or animal food system.

CFIA says the animal's birth farm has been identified, and an investigation is under way. It reported that the age and location of the infected animal are consistent with previous cases detected in Canada.

This case will be investigated just as the 15 cases before it were. Infected feed was blamed for most of the earlier cases.

Reuters Canada has a story here.

Kentucky County Steps Up To Pay Unfunded Mandate From Federal Government's New BSE Rule

 As we say out West, "This isn't our first rodeo."  So when it comes to regulations we are always interested in what happens in the actual implementation of new rules and whether or not there are any unintended consequences.

That is why we are watching for impacts of the the new so-called "BSE" rule requiring livestock renderers and animal feed manufacturers to remove the brain and spinal cord from cows 30 months and older.    We reported on the delay to June 26th for implementing the new rule here.

What has us interested is the fact that the rule applies to the disposal of dead cows, horses, pigs, goats and whatever by renderers.   How this is going to impact rural America remains to be seen.

 

Montgomery County, KY is stepping up with a long-time solution. County government has decided to continue its service of disposing of dead animals for free.

They figure taxpayers won't mind paying for the service as it will both prevent any nasty night-time disposal practices and preserve the rural, horse-ranching countryside.

 

 

 Mark Hicks, writing in the Clarksville, Ky Leaf Chronicle today, reports that:

Other than farmers, not many people think about how to dispose of a dead cow or horse that would likely weigh more than 1,000 pounds.

"It's a valuable service," Palmyra farmer Bobby Wall said. "It's more practical to have the cattle removed. It cuts down on the odor and the buzzards don't take everything — they leave bones and other pieces."

Extension Agent John Bartee lobbied Commissioners to continue the service after the BSE rule takes effect even though it will cost the Montgomery County twice as much once the new rule is in place.  Check out The Leaf Chronicle story here.

 

Alberta Prion Research Institute Good On "The Basics"

A couple of items on the Alberta Prion Research Institute's website recently caught our attention.

First, we found its "Prion Basics" a great feature, especially the listing of the various prion diseases and the mammals they affect. (See below).   Second, we wanted to call attention to the open competition the Institute has for prion research.  Deadlines are coming up, and awards of up to $150,000 sound pretty good even if paid in Canadian funds.   Go here for more.   From "the basics:"

Prion diseases are transmissible—from host to host of a single species and sometimes from one species to another—and destroy brain tissue giving it a spongy appearance. For these reasons, prion diseases are also called transmissible spongiform encephalopathies or TSEs.

Some examples of prion disease and the mammals they affect are:

  • Creutzfeldt-Jakob disease (CJD; humans)
  • variant Creutzfeldt-Jakob disease (vCJD; humans, acquired from cattle with BSE)
  • Bovine Spongiform Encephalopathy (BSE, a.k.a. mad cow disease)
  • Chronic Wasting disease (CWD; elk, deer)
  • Scrapie (infectious disease of sheep and goats)
  • Kuru (infectious, in humans who practiced cannibalism in Papua New Guinea)
  • Gerstmann-Sträussler-Scheinker disease (inherited disease of humans)
  • Fatal Familial Insomnia (inherited disease of humans)

For more from "The Basics," go here.

 

Remember When Mad Cow Disease Was Going To Kill 500,000 In Britain Alone?

 Leave it to the Wall Street Journal's Bret Stephens to remind us of "the "mad cow" panic that gripped the world in the 1990s. In his 1997 book "Deadly Feasts," Richard Rhodes warned that the human variant of mad cow, known as vCJD, might kill as many as 500,000 people a year in Britain alone. So far, total confirmed cases world-wide run to around 150."

Stephens writes the WSJ's "Global View" column and serves on the newspaper's editorial board. In"Swine Flu Hysteria" written for publication on May 5th, he writes:

In the matter of swine flu -- and the single dumbest response to it yet -- first prize was about to go to the government of Egypt, which last week ordered a cull of the country's estimated 400,000 pigs, never mind that the disease, name notwithstanding, is mainly transmitted human-to-human.

His runners-up are:

  • Russia, which used the flu panic to ban pork imports from Spain and Canada;
  • U.S. immigration restrictionists, who see in the "Mexican flu" a fresh reason to argue for a wall along the border;
  • and of course Vice President Joe Biden.

We shall continue to cover Mad Cow disease here, and we are happy not to be reporting about a pandemic.  And to be fair to Richard Rhodes, the cannibalistic recycling of animals he wrote about has been largely regulated away.

Check out the rest of Mr. Stephens' column here.